How to treat hemophilia b?
Hemophilia is one of those illnesses that sounds like it should be a superpower. Unfortunately, it’s not. It’s actually quite the opposite.
What is Hemophilia B?
For those who don’t know, hemophilia B is a blood disorder where your body doesn’t produce enough clotting factor IX. What does that mean for you? Well, it means if you bleed, way too much blood comes out and takes forever to stop. And we’re talking about anything from a paper cut to any severe injury here.
So what can you do about this?
Lucky for all my fellow hemophiliacs, there are lots of treatments available! Before we get started though…I’m not a doctor or medical professional; please talk to your doctor before trying out any new treatment methods.
Factor Replacement Therapy
Factor replacement therapy involves injecting missing clotting factors back into your body.
Typically given intravenously (IV), clotting products used in this process vary depending on how purified they’ve been and whether they’ve got recombinant or plasma-derived versions of the product.
The most common brand names include:
– BeneFIX
– Alprolix
– Rixubis
And as always with medications and doctors instructions check first, sometimes there may be side effects.
Desmopressin (DDAVP)
If missing only mild amounts of factor IX DDAVP could raise levels high enough so clots form more easily.
Desmopressin comes in two administration options:
1) Intravenous injection at the hospital/clinic – this dose lasts approximately eight hours max before administered again.
PRO TIP: Bring something fun! While I was receiving desmopressin injections every few weeks in college between classes once with three close friends we played poker making sure no one would win instantly but rather build the pot for two long periods of time. It made taking missing out on college life alot more fun!
2) Nasal spray – this isn’t FDA approved as a treatment method for Hemophilia B, so you should talk to your doctor about using it.
Surgical Options
If factor replacement operations and desmopressin can’t stop too much bleeding, further surgical measures may be necessary:
Prophylactic Surgery
Prophylactic surgery is pre-emptive actions by removing certain tissue(s). The surgery aims e.g., reducing liver-based production of clotting factors that order the injection or infusion frequency requirements’ reduction.
Joint Replacement Surgeries
Hemophiliacs are susceptible to repeated internal bleeding in their joints (hemarthrosis), resulting over time in permanent damage or expected joint replacements. Joint replacement procedures alleviate harsh arthritic symptoms like stiffness and pain while dramatically enhancing mobility.
Gene Therapy
Gene therapy has come an incredible way since 2017 when scientists developed Spark Therapeutics’ gene therapy drug named SPK-9001 which enabled patients with Haemophilia B to produce significantly increased quantities of functional blood clotting protein factor IX from one 45-minute intravenous (IV) infusion.
This brand new medical technology replaces mutated genes incapable of producing coagulation proteins with other intact genes engineered into living cells within laboratory environments.
Patients are not required daily treatment management after receiving gene administration because the medicinal effects last indefinitely without degrading over time effectively providing immunity to ordinary injuries.
Due its inherent novelty though regulatory restrictions limit global access making it exceptionally expensive; cost between $100k-$150k before insurance coverage negating affordability for most households.
So those were a few methods/choices available but always remember that every body’s situation is unique (also called YMMV) so always have your physician help guide you through anything complicated. So take care to talk to your doctor, avoid complications with not following specific steps and hopefully one day this article won’t matter because Hemophilia B cured as common cold is today!.
Hey there, I’m Dane Raynor, and I’m all about sharing fascinating knowledge, news, and hot topics. I’m passionate about learning and have a knack for simplifying complex ideas. Let’s explore together!
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